HCY 1 and 2: Homocystinuria Diet

HCY 1 and 2

HCY 1 and HCY 2 are infant formula and medical food powders that are free of the essential amino acid methionine for infants, toddlers, children, and adults with homocystinuria.

For Stages:
  • Special Dietary Needs

HCY 1 and HCY 2 are infant formula and medical food powders that are free of the essential amino acid methionine for infants, toddlers, children, and adults with homocystinuria.

HCY 1

HCY 1 is an iron-fortified infant formula and medical food powder that is free of the essential amino acid methionine for infants and toddlers with homocystinuria.

HCY 1 provides all other essential amino acids, as well as nonessential amino acids, carbohydrates, fat, essential fatty acids, vitamins, and minerals. HCY refers to homocysteine.

  • DHA and ARA
  • Methionine-free
  • Added cystine
  • Vitamin and mineral levels meet the U.S. Infant Formula Act requirements per 100 Calories
  • Increased levels of B vitamins, compared to routine infant formulas, for cofactor production
  • Vanilla scent
  • Mixes easily and stays in suspension well
  • Increased level of choline, an essential nutrient important for brain development and the normal functioning of cells

HCY 1 should only be used under the direct and continuing supervision of a doctor.

Ask your doctor if HCY 1 may be right for your baby.

Call 1-800-BABY123 for more information or to order this metabolic formula.

This product is also available at drugstore.com.

HCY 2

HCY 2 is a medical food powder that is free of the essential amino acid methionine for children and adults with homocystinuria.

HCY 2 provides all other essential amino acids as well as nonessential amino acids, carbohydrates, fat, essential fatty acids, vitamins, and minerals.

  • Methionine-free
  • Cystine level is similar to the sum of cystine and methionine found in cow's milk
  • 22 g protein equivalents/100 g powder
  • Suitable for someone with lactose intolerance
  • Vanilla scent
  • Can be easily modified with preferred flavor enhancers
  • Mixes easily and stays in suspension well
  • Vitamin and mineral levels appropriate for children and adults

HCY 2 should only be used under the direct and continuing supervision of a doctor.

Ask your doctor about if HCY 2 is right for you or your child.

Call 1-800-BABY123 for more information or to order this metabolic formula.

This product is also available at drugstore.com.

Nutrients & Ingredients

Powder

NUTRIENTS per 100 g Powder

CALORIES
 
500
PROTEIN EQUIVALENTS
g*
16.2
FAT
g
26
CARBOHYDRATE
g
51
LINOLEIC ACID
mg
4500

VITAMINS

A
IU
1520
D
IU
380
E
IU
10
K
mcg
40
THIAMIN (B1)
mcg
1000
RIBOFLAVIN (B2)
mcg
1000
B6
mcg
1000
B12
mcg
2
NIACIN
mcg
10000
FOLIC ACID (FOLACIN)
mcg
100
PANTOTHENIC ACID
mcg
3800
BIOTIN
mcg
38
C (ASCORBIC ACID)
mg
60
CHOLINE
mg
124
INOSITOL
mg
86

MINERALS

CALCIUM
mg
660
PHOSPHORUS
mg
440
MAGNESIUM
mg
66
IRON
mg
9.6
ZINC
mg
8.6
MANGANESE
mcg
380
COPPER
mcg
860
IODINE
mcg
76
SELENIUM
mcg
14.1
SODIUM
mg
240
POTASSIUM
mg
560
CHLORIDE
mg
430

*WARNING: This protein is incomplete since it does not contain the essential amino acid methionine.

INGREDIENTS: CORN SYRUP SOLIDS, VEGETABLE OIL (PALM OLEIN OIL, COCONUT OIL, SOY OIL, HIGH OLEIC SUNFLOWER OIL), AMINO ACIDS (L-GLUTAMINE, L-LEUCINE, POTASSIUM ASPARTATE, L-LYSINE HYDROCHLORIDE, L-PROLINE, L-VALINE, L-ISOLEUCINE, L-ALANINE, L-ARGININE, L-THREONINE, L-PHENYLALANINE, L-TYROSINE, L-SERINE, L-CYSTINE, GLYCINE, L-HISTIDINE, L-TRYPTOPHAN), MODIFIED CORN STARCH, SUGAR, CALCIUM PHOSPHATE, AND LESS THAN 1%: MORTIERELLA ALPINA OIL**, CRYPTHECODINIUM COHNII OIL***, ETHYL VANILLIN, SODIUM CITRATE, POTASSIUM CITRATE, MAGNESIUM OXIDE, FERROUS SULFATE, POTASSIUM CHLORIDE, ZINC SULFATE, CUPRIC SULFATE, MANGANESE SULFATE, SODIUM IODIDE, SODIUM SELENITE), CHOLINE CHLORIDE, INOSITOL, ASCORBIC ACID, NIACINAMIDE, CALCIUM PANTOTHENATE, VITAMIN B6 HYDROCHLORIDE, THIAMIN HYDROCHLORIDE, RIBOFLAVIN, VITAMIN D3, FOLIC ACID, BIOTIN, VITAMIN K1, VITAMIN E ACETATE, VITAMIN A PALMITATE, VITAMIN B12, TAURINE, L-CARNITINE.

**A SOURCE OF ARACHIDONIC ACID (ARA)
***A SOURCE OF DOCOSAHEXAENOIC ACID (DHA)

Please refer to your product packaging for the most accurate information.

Last Updated: 12/30/11

NUTRIENTS per 100 g Powder

CALORIES
 
410
PROTEIN EQUIVALENTS
g*
22
FAT
g
8.5
CARBOHYDRATE
g
61

VITAMINS

A
IU
1730
D
IU
350
E
IU
12.2
K
mcg
47
THIAMIN (B1)
mcg
1430
RIBOFLAVIN (B2)
mcg
1140
B6
mcg
1140
B12
mcg
2.9
NIACIN
mcg
26000
FOLIC ACID (FOLACIN)
mcg
410
PANTOTHENIC ACID
mcg
5700
BIOTIN
mcg
57
C (ASCORBIC ACID)
mg
57
CHOLINE
mg
98
INOSITOL
mg
57

MINERALS

CALCIUM
mg
730
PHOSPHORUS
mg
730
MAGNESIUM
mg
163
IRON
mg
13.8
ZINC
mg
13.8
MANGANESE
mcg
1500
COPPER
mcg
1430
IODINE
mcg
63
SELENIUM
mcg
33
CHROMIUM
mcg
45
MOLYBDENUM
mcg
45
SODIUM
mg
590
POTASSIUM
mg
1100
CHLORIDE
mg
960

*WARNING: This protein is incomplete since it does not contain the essential amino acid methionine.

INGREDIENTS: CORN SYRUP SOLIDS, AMINO ACIDS (L-GLUTAMINE, L-LEUCINE, L-LYSINE HYDROCHLORIDE, POTASSIUM ASPARTATE, L-PROLINE, L-VALINE, L-ISOLEUCINE, L-ALANINE, L-ARGININE, L-THREONINE, L-PHENYLALANINE, L-TYROSINE, L-SERINE, L-CYSTINE, GLYCINE, L-HISTIDINE, L-TRYPTOPHAN), SUGAR, SOY OIL, MODIFIED CORN STARCH, CALCIUM PHOSPHATE, SODIUM CITRATE, MAGNESIUM PHOSPHATE, POTASSIUM CHLORIDE, AND LESS THAN 1%: SODIUM PHOSPHATE, POTASSIUM CITRATE, CHOLINE CHLORIDE, ASCORBIC ACID, TAURINE, INOSITOL, FERROUS SULFATE, L-CARNITINE, ZINC SULFATE, NIACINAMIDE, VITAMIN E ACETATE, VITAMIN A PALMITATE, CALCIUM PANTOTHENATE, CUPRIC SULFATE, MANGANESE SULFATE, VITAMIN B12, THIAMIN HYDROCHLORIDE, VITAMIN B6 HYDROCHLORIDE, RIBOFLAVIN, FOLIC ACID, VITAMIN D3, CHROMIC CHLORIDE, SODIUM MOLYBDATE, SODIUM SELENITE, SODIUM IODIDE, BIOTIN, VITAMIN K1, ETHYL VANILLIN.

Please refer to your product packaging for the most accurate information.

Last Updated: 2/13/12

Preparation

Powder

Mead Johnson Nutrition HCY 1 is to be used only in the dietary management of infants and young children with documented homocystinuria while under direct and continuing medical supervision.

WARNING: This product is nutritionally incomplete. Care must be taken to provide enough methionine to support growth using other foods with this amino acid as required. Medical professionals must carefully and constantly supervise use of HCY 1 with other foods and liquids and adjust the diet based on frequent blood tests.

INSTRUCTIONS FOR PREPARATION AND USE

Your child’s health depends on carefully following the instructions below. Proper hygiene, preparation, dilution, use and storage are important when preparing product. Powdered products are not sterile and should not be fed to premature infants or persons who might have immune problems unless directed and supervised by your child’s medical professional.

Ask your baby’s medical professional about the need to use cooled, boiled water for mixing and the need to boil clean utensils, bottles and nipples in water before use.
Your baby’s medical professional will provide instructions for the correct amounts of water and powder*. Pour the required amount of water into the bottle. Add the correct amount of powder, cap the bottle and shake vigorously.

*If instructed to use the scoop in the can, each scoop (unpacked and leveled) delivers approximately 4.5 g of powder. Store the DRY scoop in this can.

Failure to follow these instructions could result in severe harm. Once prepared, product can spoil quickly. Either feed immediately or cover and store in refrigerator at 35-40°F (2-4°C) for no longer than 24 hours. Do not use prepared product if it is unrefrigerated for more than a total of 2 hours. Do not freeze prepared product. After feeding begins, use product within one hour or discard.

WARNING: Do not use a microwave oven to warm product. Serious burns may result.

POWDER STORAGE: Store cans at room temperature. After opening can, keep tightly covered, store in a dry area and use contents within 1 month. Do not freeze powder and avoid excessive heat.

USE BY DATE ON BOTTOM OF CAN.

WARNING: Not for parenteral (I.V.) use.

Last Updated: 12/29/11

Mead Johnson Nutrition HCY 2 is to be used only in the dietary management of children and adults with documented homocystinuria while under direct and continuing medical supervision.

WARNING: This product is nutritionally incomplete. Continuing medical supervision and frequent blood tests are required. HCY 2 must be supplemented using other food sources of protein and fluid to provide enough methionine to support dietary requirements of children and adults.

INSTRUCTIONS FOR PREPARATION AND USE

Your medical professional will provide the correct amount of powder to mix with water for consumption.*

It is important to follow the directions below.

Measure the correct amount of water into a suitable container for mixing. Then add the required amount of HCY 2. Mix well until blended. Consume the prepared beverage immediately or cover and refrigerate. Use within 48 hours of preparation. Mix before drinking.

*If instructed to use the scoop in the can, each unpacked, level scoop delivers approximately 14.5 g of powder. Store the DRY scoop in this can.

POWDER STORAGE: Store cans at room temperature. After opening can, keep tightly covered, store in a dry area and use contents within 1 month. Do not freeze powder and avoid excessive heat.

USE BY DATE ON BOTTOM OF CAN.

WARNING: Not for parenteral (I.V.) use.

Last Updated: 2/13/12

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